Asian Journal of Case Reports in Surgery

The Perils of Laparoscopic Cholecystectomy in a Patient with Christmas Disease

Udit Bagchi

Department of General Surgery, SCB Medical College, Cuttack, Odisha, India.

Suraj Ethiraj *

Department of General Surgery, SCB Medical College, Cuttack, Odisha, India.

Soumith Subhash

Bokaro General Hospital, Bokaro, India.

*Author to whom correspondence should be addressed.

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Abstract

Surgical procedures in hemophiliacs require a combined and multidisciplinary approach from both the surgeon and haematologist. This report is of a successful laparoscopic cholecystectomy in a patient with haemophilia B. We describe a 34 year old male, known case of factor 9 deficiency with gall stone disease undergoing cholecystectomy with adequate pre and post operative optimisation. Challenges in such patients include deranged clotting time, high risk of bleeding in the perioperative period. These cases should be approached with caution and performed in high volume centres with experienced team of surgeons and haematologists.

Keywords: Laparoscopic cholecystectomy, haemophilia B, coagulopathy, factor IX deficiency

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